Table 1 TMA/aHUS scoring system

TMA score (a)

Hb < 10.0 g/dL^a

3

PLT < 150 × 10⁹/L

3

Renal failure^b

2

Extrarenal organ failures^c

2

Possible range

0 to 10

Positive aHUS score (b)^d

Past history of TMA

1 time

1

 ≥ 2 times

3

Family history of TMA

1 family member

1

 ≥ 2 family member

3

Age at onset

 < 63 years

1

 < 10 years

3

Trigger^e

1

Possible range

0 to 10

Exclusion aHUS score (c)

Bloody stool

 − 3

ADAMTS13 < 10%

 − 3

Underlying diseases^f

 − 3

D-dimer^g > 20 μg/mL

 − 3

WBC^h > 16,000/mL

 − 3

Possible range

 − 15 to 0

TMA/aHUS score

 = a + b + c

 − 15 to 20